Dandy walker syndrome is a brain deformity present at birth consisting of a deformity of the cerebellum and the presence of the cyst in the lower portion of the brain. The deformity involves an area in the back of the brain that controls movements and cognitive learning. In some cases, there is the abnormal accumulation of cerebrospinal fluid within the ventricle of the vein. The symptoms of this syndrome may develop suddenly or may go unnoticed, which often occur in early infancy resulting in the slow motor development and progressive enlargement of the skull.
Dandy Walker syndrome is frequently associated with the disorder of other areas of the central nervous system, including an absence of the area made up of nerve fibers connecting the two cerebral hemispheres i.e corpus callosum and malformation of the heart, face, limbs, fingers, and toes.
What Are The Causes Of Dandy-Walker Syndrome?
This syndrome occurs during brain development before birth. An exact cause is unknown; it is likely a combination of genetic and environmental factors.
• Impaired development of normal speech and language.
• Slow motor development
• Lack of muscle coordination
• Increase had circumference
• Jerky eye movements
• Bulging of the back of the skull
• Abnormal breathing
• Malformation of heart, kidney
• Urinary tract abnormality
• Oral-facial clefts
• Extra digits
• Nerves problem that controls the eyes, face, and neck
• Complete case history
• Physical examination and observation.
• Antenatal ultrasound
• CT and MRI scan
• Surgery: surgical procedure known as shunt may be required to drain off excess fluid within the brain, which will lead to reduce intracranial pressure and help control swelling.
• Ventriculostomy: a tube from one ventricle to another. It allows extra fluid to drain out of the affected ventricle.
• Prophylactic treatment of malformations
Prognosis of Dandy-walker syndrome is variable. In some cases, children have normal cognition and others never achieve normal intellectual development even if a condition is treated early. Longevity depends on the severity of the syndrome and associated malformation.
• Take care of child with symptoms like seizures etc
• Genetic counseling of parents
• Make your child sited in the area where there are no sharp edges.
• Hold/support while walking.
• Speech therapy may help a bit in older children.
• One half of the body is convulsed, other half is paralyzed.
• Strabismus rapid and weak pulse and scanty urine.
• Child very drowsy and accumulation of fluid in the brain
• Dull, heavy sensation in the occiput.
• Heat, throbbing, pressing pains, better with pressure.
• Vertigo with sneezing, worse on lying down or closing the eyes
• Pain worse light, noise jar, laying down and in the afternoon.
• Better by pressure and in semi-erect posture.
• Sensitive to least touch
• Vertigo, with falling to the left side or backward.
• Boring of a head into the pillow, drawn backward and rolls from side to side.
• Constant moaning.
• A headache worse on the right side and on lying down, ill effects of cold and from the haircut.
• A sense of weight on top of the head.
• A headache, with cold hand and feet.
• Vertigo on ascending and on turning the head.
• A headache from over lifting, from mental exertion with nausea.
• Head feels hot and heavy with a pale face.
• Open fontanelles; head enlarged, much perspiration, wet the pillow.
• Forehead wrinkles in folds.
• Rolls head day and night, moaning, sudden screams.
• Bores head into the pillow beats it with hands.
• Dull pain in occiput with a sensation of water swashing inside.
• A headache culminates in vomiting.
• Feels as if he would fall to the left side.
• Rolls head from side to side.
• Bores head into the pillow.
• Occipital pain, with weight on the vertex.
• Automatic motion of head and hands.
• Brainfag, headache in overtaxed school children.
• Forehead cool, a base of brain hot.
• Roaring in the head.
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